文章摘要

IgG4相关性涎腺炎的临床病理特点

作者: 1葛莉, 1冯瑞娥
1 中国医学科学院,北京协和医学院,北京协和医院病理科,北京100730
通讯: 冯瑞娥 Email: FengRE@pumch.cn
DOI: 10.3978/j.issn.2095-6959.2013.03.016

摘要

IgG4相关性疾病作为一种全身系统性疾病,可累及多个器官及组织。发生于涎腺的IgG4相关性涎腺炎容易与干燥综合征、慢性非特异性涎腺炎、淋巴瘤等多种疾病混淆,延误治疗并给患者带来诸多不必要的手术负担。因此有必要提高对IgG4相关性涎腺炎的认识。本文就IgG4相关性涎腺炎的临床及病理组织学等特点进行综述。
关键词: IgG4相关性疾病;IgG4相关性涎腺炎;临床病理特点

Clinicopathological features of IgG4-related sialadenitis

Authors:

CorrespondingAuthor: FENG Ruie Email: FengRE@pumch.cn

DOI: 10.3978/j.issn.2095-6959.2013.03.016

Abstract

Immunoglobubin G4-related disease (IgG4-RD) is an emerging disease with unknown etiology and multiorgan involvement. IgG4-related sialadenitis is easily to be misdiagnosed as Sjögren’s syndrome, chronic nonspecific sialadenitis, or lymphoma. Thus many patients cannot be treated timely and even undergo many unnecessary surgery. It is important to improve our knowledge on IgG4-related sialadenitis. In this review, we summarized the clinicopathological characteristics of IgG4-related sialadenitis.

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