囊性纤维化跨膜调节因子与非囊性纤维化肺部疾病关系的研究进展
@article{LCBL12096, author = {梦鸽 李 和 建文 毛}, title = {囊性纤维化跨膜调节因子与非囊性纤维化肺部疾病关系的研究进展}, journal = {临床与病理杂志}, volume = {37}, number = {6}, year = {2017}, keywords = {}, abstract = {囊性纤维化跨膜调节因子(cystic fibrosis transmembrane regulatory factor,CFTR)是一种跨膜蛋白质,也是一种重要的离子通道。囊性纤维化(cystic fibrosis,CF)是一种具有家族常染色体隐性遗传的先天性疾病,CFTR基因突变使其编码的CFTR蛋白功能缺陷从而导致囊性纤维化的发生。CFTR与非囊性纤维化肺部疾病如肺水肿、急性呼吸窘迫综合征和气道上皮损伤等的发生发展密切相关。}, url = {https://lcbl.amegroups.com/article/view/12096} }