IgG4相关血管疾病的研究进展
| 作者: |
1白亮亮,
1刘秀梅
1 山西医科大学第一医院风湿免疫科，太原 030001 |
| 通讯: |
刘秀梅
Email: liuxiumei@medmail.com.cn |
| DOI: | 10.3978/j.issn.2095-6959.2021.01.029 |
摘要
IgG4相关疾病是一种自身免疫性疾病，常累及全身多部位的组织及器官。IgG4相关的血管炎常侵犯多部位的血管，以主动脉及其一级分支为主，并容易合并动脉瘤，动脉瘤的破裂会有致命风险。在诊断上，需鉴别IgG4相关的血管炎与其他常见血管炎；在治疗上，激素虽然是治疗IgG4相关的血管炎的基石，但也会加快某些患者血管瘤的破裂，因此，临床上需结合介入及外科手术等方法综合治疗。
关键词：
IgG4相关疾病；血管炎；动脉瘤；诊断；治疗
Research progress in IgG4 related vascular diseases
CorrespondingAuthor: LIU Xiumei Email: liuxiumei@medmail.com.cn
DOI: 10.3978/j.issn.2095-6959.2021.01.029
Abstract
IgG4-related disease is an autoimmune disease that often affects tissues and organs in many parts of the body. IgG4-related vasculitis often involves multiple vessels, mainly the aorta and its primary branches, and is prone to aneurysm rupture with a fatal risk. In terms of diagnosis, IgG4-related vasculitis should be differentiated from other common vasculitis. In terms of treatment, although hormone is the cornerstone for the treatment of IgG4-related vasculitis, it can also accelerate the rupture of hemangioma in some patients. Therefore, clinical comprehensive treatment should be combined with interventional and surgical methods.
Keywords：
IgG4 related diseases; vasculitis; aneurysm; diagnosis; treatment